Taussig-Bing syndrome
Encyclopedia
Taussig-Bing syndrome is a cyanotic
congenital heart defect
(CHD) in which the patient has both double outlet right ventricle
(DORV) and subpulmonic ventricular septal defect
(VSD).
In DORV, instead of the normal situation where blood from the left ventricle
(LV) flows out to the aorta
and blood from the right ventricle
(RV) flows out to the pulmonary artery
, both aorta
and pulmonary artery
are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is subpulmonic (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.
The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of dextro-Transposition of the great arteries
(but the surgical repair is different). It can be corrected surgically also with the arterial switch operation (ASO).
Cyanotic heart defect
A cyanotic heart defect is a group-type of congenital heart defects . The patient appears blue , due to deoxygenated blood bypassing the lungs and entering the systemic circulation...
congenital heart defect
Congenital heart defect
A congenital heart defect is a defect in the structure of the heart and great vessels which is present at birth. Many types of heart defects exist, most of which either obstruct blood flow in the heart or vessels near it, or cause blood to flow through the heart in an abnormal pattern. Other...
(CHD) in which the patient has both double outlet right ventricle
Double outlet right ventricle
Double outlet right ventricle is a form of congenital heart disease where both of the great arteries connect to the right ventricle...
(DORV) and subpulmonic ventricular septal defect
Ventricular septal defect
A ventricular septal defect is a defect in the ventricular septum, the wall dividing the left and right ventricles of the heart.The ventricular septum consists of an inferior muscular and superior membranous portion and is extensively innervated with conducting cardiomyocytes.The membranous...
(VSD).
In DORV, instead of the normal situation where blood from the left ventricle
Left ventricle
The left ventricle is one of four chambers in the human heart. It receives oxygenated blood from the left atrium via the mitral valve, and pumps it into the aorta via the aortic valve.-Shape:...
(LV) flows out to the aorta
Aorta
The aorta is the largest artery in the body, originating from the left ventricle of the heart and extending down to the abdomen, where it branches off into two smaller arteries...
and blood from the right ventricle
Right ventricle
The right ventricle is one of four chambers in the human heart. It receives deoxygenated blood from the right atrium via the tricuspid valve, and pumps it into the pulmonary artery via the pulmonary valve and pulmonary trunk....
(RV) flows out to the pulmonary artery
Pulmonary artery
The pulmonary arteries carry deoxygenated blood from the heart to the lungs. They are the only arteries that carry deoxygenated blood....
, both aorta
Aorta
The aorta is the largest artery in the body, originating from the left ventricle of the heart and extending down to the abdomen, where it branches off into two smaller arteries...
and pulmonary artery
Pulmonary artery
The pulmonary arteries carry deoxygenated blood from the heart to the lungs. They are the only arteries that carry deoxygenated blood....
are connected to the RV, and the only path for blood from the LV is across the VSD. When the VSD is subpulmonic (sitting just below the pulmonary artery), the LV blood then flows preferentially to the pulmonary artery. Then the RV blood, by default, flows mainly to the aorta.
The clinical manifestations of a Taussig-Bing anomaly, therefore, are much like those of dextro-Transposition of the great arteries
Dextro-Transposition of the great arteries
dextro-Transposition of the great arteries , sometimes also referred to as complete transposition of the great arteries, is a birth defect in the large arteries of the heart...
(but the surgical repair is different). It can be corrected surgically also with the arterial switch operation (ASO).