Ackerman syndrome
Encyclopedia
Ackerman syndrome is a familial syndrome
of fused molar roots with a single canal (taurodontism
), hypotrichosis
, full upper lip without a cupid’s bow, thickened and wide philtrum
, and occasional juvenile glaucoma
.
It can also refer to interstitial granulomatous dermatitis
.
Syndrome
In medicine and psychology, a syndrome is the association of several clinically recognizable features, signs , symptoms , phenomena or characteristics that often occur together, so that the presence of one or more features alerts the physician to the possible presence of the others...
of fused molar roots with a single canal (taurodontism
Taurodontism
Taurodontism is a condition found in molar teeth where the body of the tooth and pulp chamber is enlarged vertically at the expense of the roots. As a result, the floor of the pulp and the furcation of the tooth is moved apically down the root...
), hypotrichosis
Hypotrichosis
Hypotrichosis is a condition of abnormal hair patterns - predominantly loss or reduction. It occurs, most frequently, by the growth of vellus hair in areas of the body that normally produce terminal hair. Typically, the individual's hair growth is normal after birth, but shortly thereafter the hair...
, full upper lip without a cupid’s bow, thickened and wide philtrum
Philtrum
The philtrum , is a medial cleft common to many mammals, extending from the nose to the upper lip, and, together with a glandular rhinarium and slit-like nostrils, is believed to constitute the primitive condition for mammals in general...
, and occasional juvenile glaucoma
Glaucoma
Glaucoma is an eye disorder in which the optic nerve suffers damage, permanently damaging vision in the affected eye and progressing to complete blindness if untreated. It is often, but not always, associated with increased pressure of the fluid in the eye...
.
It can also refer to interstitial granulomatous dermatitis
Dermatitis
-Etymology:Dermatitis derives from Greek derma "skin" + -itis "inflammation" and genetic disorder.-Terminology:There are several different types of dermatitis. The different kinds usually have in common an allergic reaction to specific allergens. The term may describe eczema, which is also called...
.